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Case reports in pediatrics 81건

  1. [해외논문]   Scapular Bronchogenic Cyst in a Girl Presenting as Recurrent Cellulitis: A Case Report and Review of the Literature  

    Mir, Zuhaib M. (Department of Surgery, Division of General Surgery, Queen's University and Kingston Health Sciences Centre, 76 Stuart Street, Kingston, ON, Canada ) , Wang, Ami (Department of Pathology and Molecular Medicine, Queen's University and Kingston Health Sciences Centre, 76 Stuart Street, Kingston, ON, Canada ) , Winthrop, Andrea (Department of Surgery, Division of General Surgery, Queen's University and Kingston Health Sciences Centre, 76 Stuart Street, Kingston, ON, Canada ) , Kolar, Mila (Department of Surgery, Division of General Surgery, Queen's University and Kingston Health Sciences Centre, 76 Stuart Street, Kingston, ON, Canada)
    Case reports in pediatrics v.2018 ,pp. 1 - 4 , 2018 , 2090-6803 ,

    초록

    Bronchogenic cysts are rare, congenital cysts originating from respiratory epithelium and typically found within the chest. Cutaneous bronchogenic cysts are exceedingly uncommon, with only 19 reported cases in the scapular region and almost exclusively occurring in male patients. Herein, we present the case of a female patient with recurrent cellulitis secondary to a bronchogenic cyst, which was diagnosed after surgical excision. We also provide a review of the literature to consolidate the current understanding of cutaneous scapular bronchogenic cysts. To our knowledge, this is the first such case reported from Canada.

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    회원님의 원문열람 권한에 따라 열람이 불가능 할 수 있으며 권한이 없는 경우 해당 사이트의 정책에 따라 회원가입 및 유료구매가 필요할 수 있습니다.이동하는 사이트에서의 모든 정보이용은 NDSL과 무관합니다.

    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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    Fig. 1 이미지
  2. [해외논문]   Asymmetric Omphalopagus in a Triplet after In Vitro Fertilization: A Rare Case of Conjoined Twinning  

    Jabari, Samir (Institute of Anatomy and Cell Biology, Faculty of Medicine, Friedrich-Alexander-University Erlangen-Nürnberg, Erlangen, Germany ) , Carbon, Roman (Department of Pediatric Surgery, Faculty of Medicine, Friedrich-Alexander-University Erlangen-Nürnberg, Erlangen, Germany ) , Besendö (Department of Pediatric Surgery, Faculty of Medicine, Friedrich-Alexander-University Erlangen-Nürnberg, Erlangen, Germany ) , rfer, Manuel (Institute of Pathology, Faculty of Medicine, Friedrich-Alexander-University Erlangen-Nürnberg, Erlangen, Germany ) , Hartmann, Arndt (Department of Radiology, Faculty of Medicine, Friedrich-Alexander-University Erlangen-Nürnberg, Erlangen, Germany ) , Rompel, Oliver (Department of Pediatrics, Faculty of Medicine, Friedrich-Alexander-University Erlangen-Nürnberg, Erlangen, Germany ) , Hoerning, André (Institute of Pathology, Faculty of Medicine, Friedrich-Alexander-University Erlangen-Nürnberg, Erlangen, Germany) , , Sö , der, Stephan
    Case reports in pediatrics v.2018 ,pp. 1 - 5 , 2018 , 2090-6803 ,

    초록

    Introduction . Asymmetric omphalopagus is a rare situation of conjoined twinning, in which a grossly defective twin is attached to the thorax and upper abdomen of the main twin. We describe a case of an asymmetric omphalopagus accompanied by a normal triplet after assisted reproductive technology (ART) and tried to further characterize the all aspects of the conjoined twins. Case Presentation : Perioperative diagnostic imaging was carried out followed by an autopsy to evaluate all aspects of the parasite accompanied by histological, immunohistochemical, and molecular biological evaluation. The parasite had well-developed lower extremities as well as upper extremities with a cleft hand syndrome. The sex was nondeterminable, but DNA fingerprinting revealed that both parasite and autosite are monozygotic, so are females. There was no sign of any axial skeleton or central nervous system. We found a rudimentary rectum with a nonpervious anus, a kidney, ureter, urinary bladder, and a blind-ending urethra. The blood supply of the parasite was connected to the vessel system of the autosite. Conclusions . To our knowledge, only two cases of parasitic omphalopagus after ART have been described to date. Altogether, 52 cases have been reported, and in most of them, the parasites were successfully separated.

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    회원님의 원문열람 권한에 따라 열람이 불가능 할 수 있으며 권한이 없는 경우 해당 사이트의 정책에 따라 회원가입 및 유료구매가 필요할 수 있습니다.이동하는 사이트에서의 모든 정보이용은 NDSL과 무관합니다.

    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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  3. [해외논문]   Type IV Laryngotracheoesophageal Cleft Associated with Type III Esophageal Atresia in 1p36 Deletions Containing the RERE Gene: Is There a Causal Role for the Genetic Alteration?  

    Pelizzo, Gloria (Pediatric Surgery Unit, Pediatric Surgery Unit, Children's Hospital “G. Di Cristina”, ARNAS “Civico-Di Cristina-Benfratelli”, Palermo, Italy ) , Puglisi, Aurora (Pediatric Anesthesiology and Intensive Care Unit, Pediatric Anesthesiology and Intensive Care Unit, Children's Hospital “G. Di Cristina”, ARNAS “Civico-Di Cristina-Benfratelli”, Palermo, Italy ) , Lapi, Maria (Pediatric Anesthesiology and Intensive Care Unit, Pediatric Anesthesiology and Intensive Care Unit, Children's Hospital “G. Di Cristina”, ARNAS “Civico-Di Cristina-Benfratelli”, Palermo, Italy ) , Piccione, Maria (Department of Sciences for Health Promotion and Mother and Child Care “Giuseppe D'Alessandro”, University of Palermo, Palermo, Italy ) , Matina, Federico (Neonatal Intensive Care Unit, A.O.U.P. “P. Giaccone”, Department of Sciences for Health Promotion and Mother and Child Care “G. D'Alessandro”, Palermo, Italy ) , Busè (Department of Sciences for Health Promotion and Mother and Child Care “Giuseppe D'Alessandro”, University of Palermo, Pa) , , Martina , Mura, Giovanni Battista , Re, Giuseppe , Calcaterra, Valeria
    Case reports in pediatrics v.2018 ,pp. 1 - 5 , 2018 , 2090-6803 ,

    초록

    The causes of embryological developmental anomalies leading to laryngotracheoesophageal clefts (LTECs) are not known, but are proposed to be multifactorial, including genetic and environmental factors. Haploinsufficiency of the RERE gene might contribute to different phenotypes seen in individuals with 1p36 deletions. We describe a neonate of an obese mother, diagnosed with type IV LTEC and type III esophageal atresia (EA), in which a 1p36 deletion including the RERE gene was detected. On the second day of life, a right thoracotomy and extrapleural esophagus atresia repair were attempted. One week later, a right cervical approach was performed to separate the cervical esophagus from the trachea. Three months later, a thoracic termino-terminal anastomosis of the esophagus was performed. An anterior fundoplication was required at 8 months of age due to severe gastroesophageal reflux and failure to thrive. A causal role of 1p36 deletions including the RERE gene in the malformation is proposed. Moreover, additional parental factors must be considered. Future studies are mandatory to elucidate genomic and epigenomic susceptibility factors that underlie these congenital malformations. A multiteam approach is a crucial factor in the successful management of affected patients.

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    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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  4. [해외논문]   A Wilms' Tumor with Spinal Cord Compression: An Extrarenal Origin?  

    Petit, Audrey (Département de Pédiatrique, CHU de Grenoble, Grenoble, France ) , Rubio, Amandine (Département de Pédiatrique, CHU de Grenoble, Grenoble, France ) , Durand, Chantal (Département de Radiologie, CHU de Grenoble, Grenoble, France ) , Piolat, Christian (Département de Chirurgie, CHU de Grenoble, Grenoble, France ) , Perret, Cé (Département de Pédiatrique, CHU de Grenoble, Grenoble, France ) , cile (Département de Pédiatrique, CHU de Grenoble, Grenoble, France ) , Pagnier, Anne (Département de Pédiatrique, CHU de Grenoble, Grenoble, France ) , Plantaz, Dominique (Département de Pathologie, CHU de Grenoble, Grenoble, France) , Sartelet, Hervé
    Case reports in pediatrics v.2018 ,pp. 1 - 4 , 2018 , 2090-6803 ,

    초록

    Spinal cord compression in Wilms' tumor (WT) is an extremely rare event that can have a very poor prognosis if not taken care of rapidly. Most cases reported in the literature involve widely metastatic patient with bone or paraspinal metastases or occasionally intradural metastasis. Here, we present the case of a 3-year-old girl of WT confirmed by biopsy, with spinal cord compression due to the direct contiguous spread of a tumor through 2 vertebral foramina. Abdominal ultrasonography and magnetic resonance imaging performed for an abdominal mass revealed a large heterogeneous tumor near the upper pole of the left kidney. A nodular infiltration extended through the T11-L1 and L1-L2 neural foramina, forming an intraspinal mass that compressed the spinal cord. Major paresthesia subsequently occurred, requiring urgent treatment with corticosteroids and chemotherapy. The evolution was rapidly satisfying. After six courses of chemotherapy, a left nephrectomy was performed. Macroscopic examination identified a large tumor attached to the kidney without renal infiltration. Microscopical examination concluded to a nephroblastoma with regressive changes, of intermediate risk. Evolution at 6 months is satisfactory, with no neurological deficit. The histological aspect of the tumor and the clinical outcome suggest that she had an extrarenal WT that spread through the vertebral foramina and was secondarily attached to the kidney.

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    회원님의 원문열람 권한에 따라 열람이 불가능 할 수 있으며 권한이 없는 경우 해당 사이트의 정책에 따라 회원가입 및 유료구매가 필요할 수 있습니다.이동하는 사이트에서의 모든 정보이용은 NDSL과 무관합니다.

    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

    이미지

    Fig. 1 이미지
  5. [해외논문]   Congenital Granular Cell Tumor: Case Report and Review  

    Gardner, Preston (Department of Plastic & Reconstructive Surgery, Beaumont Hospital-Farmington Hills, 28050 Grand River Ave., Farmington Hills, MI 48336, USA ) , Rozzelle, Arlene (Department of Plastic & Reconstructive Surgery, Childrens Hospital of Michigan, Detroit Medical Center, 3901 Beaubien St., Detroit, MI 48201, USA)
    Case reports in pediatrics v.2018 ,pp. 1 - 3 , 2018 , 2090-6803 ,

    초록

    Congenital granular cell tumors are infrequently occurring masses occurring on a neonate's gingiva/alveolus. These lesions are benign with no noted malignant transformation, and treatment of excision is based on its effect on the neonate's respiratory ability and/or nutritional intake. The purpose of this review is to discuss a case of a congenital granular cell tumor and its treatment and review of the literature including demographics, histopathology, and operative treatment.

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    회원님의 원문열람 권한에 따라 열람이 불가능 할 수 있으며 권한이 없는 경우 해당 사이트의 정책에 따라 회원가입 및 유료구매가 필요할 수 있습니다.이동하는 사이트에서의 모든 정보이용은 NDSL과 무관합니다.

    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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  6. [해외논문]   Intramural Bowel Hematoma Presenting as Small Bowel Obstruction in a Patient on Low-Molecular-Weight Heparin  

    Choi, Beatrix Hyemin (Division of Pediatric Surgery, Department of Surgery, NYU School of Medicine, Hassenfeld Children's Hospital at NYU Langone, New York, NY, USA ) , Koeckert, Michael (Department of Surgery, NYU School of Medicine, NYU Langone Medical Center, New York, NY, USA ) , Tomita, Sandra (Division of Pediatric Surgery, Department of Surgery, NYU School of Medicine, Hassenfeld Children's Hospital at NYU Langone, New York, NY, USA)
    Case reports in pediatrics v.2018 ,pp. 1 - 3 , 2018 , 2090-6803 ,

    초록

    There is increasing use of low-molecular-weight heparin (LMWH) for treatment of pediatric thromboembolic disease as it has been shown to be safe and effective. It has several advantages over unfractionated heparin, such as reduced need for monitoring, easier route of administration, decreased risk of heparin-induced thrombocytopenia, and lack of drug-drug interactions. Nevertheless, LMWH still poses a bleeding risk as with any anticoagulant therapy. We present the case of a 4-year-old boy who was placed on LMWH for a catheter-related deep venous thrombosis in the setting of intractable seizures and subsequently developed a small bowel obstruction secondary to a suspected intussusception. He underwent exploratory laparotomy and was found to have an intramural bowel hematoma. Prior to this bleed, the patient had been monitored daily, and his anti-Xa levels were found to be in the therapeutic range. This case highlights the need for a high index of suspicion for spontaneous bleeding even in the setting of therapeutic anti-Xa levels.

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    회원님의 원문열람 권한에 따라 열람이 불가능 할 수 있으며 권한이 없는 경우 해당 사이트의 정책에 따라 회원가입 및 유료구매가 필요할 수 있습니다.이동하는 사이트에서의 모든 정보이용은 NDSL과 무관합니다.

    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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    Fig. 1 이미지
  7. [해외논문]   Infantile Hemangioma Presenting as Colocolic Intussusception in an Infant Case Report with Review of Pathologic Lead Points  

    Rais, Rehan (From the Lauren V. Ackerman Laboratory of Surgical Pathology, and Division of Pediatric Surgery, St. Louis Children's Hospital, Washington University Medical Center, St. Louis, MO, USA ) , Gonzá (From the Lauren V. Ackerman Laboratory of Surgical Pathology, and Division of Pediatric Surgery, St. Louis Children's Hospital, Washington University Medical Center, St. Louis, MO, USA ) , lez, Ivá (From the Lauren V. Ackerman Laboratory of Surgical Pathology, and Division of Pediatric Surgery, St. Louis Children's Hospital, Washington University Medical Center, St. Louis, MO, USA ) , n (From the Lauren V. Ackerman Laboratory of Surgical Pathology, and Division of Pediatric Surgery, St. Louis Children's Hospital, Washington University Medical Center, St. Louis, MO, USA) , Saito, Jacqueline M. , Dehner, Louis P.
    Case reports in pediatrics v.2018 ,pp. 1 - 4 , 2018 , 2090-6803 ,

    초록

    Infantile hemangioma (IH) is one of the most common vascular anomalies of early childhood and is usually recognized in the first few weeks to months of life as a solitary cutaneous lesion. This report documents our experience with a GLUT-1 positive IH presenting as the pathologic lead point in a colocolic intussusception in a 10-week-old infant who had no skin lesions. Literature suggests approximately 2% of all children presenting with an intussusception require surgical intervention; however, an IH as the pathologic lead point is unique.

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    회원님의 원문열람 권한에 따라 열람이 불가능 할 수 있으며 권한이 없는 경우 해당 사이트의 정책에 따라 회원가입 및 유료구매가 필요할 수 있습니다.이동하는 사이트에서의 모든 정보이용은 NDSL과 무관합니다.

    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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  8. [해외논문]   Delayed Diagnosis of Acute Rheumatic Fever in a Patient with Multiple Emergency Department Visits  

    Kaminecki, Inna (Department of Pediatrics, The Unterberg Children's Hospital at Monmouth Medical Center, Long Branch, NJ, USA ) , Verma, Renuka (Department of Pediatrics, The Unterberg Children's Hospital at Monmouth Medical Center, Long Branch, NJ, USA ) , Brunetto, Jacqueline (Department of Pediatrics, The Unterberg Children's Hospital at Monmouth Medical Center, Long Branch, NJ, USA ) , Rivera, Loyda I. (Department of Pediatrics, The Unterberg Children's Hospital at Monmouth Medical Center, Long Branch, NJ, USA)
    Case reports in pediatrics v.2018 ,pp. 1 - 4 , 2018 , 2090-6803 ,

    초록

    While the incidence of acute rheumatic fever (ARF) in the United States has declined over the past years, the disease remains one of the causes of severe cardiovascular morbidity in children. The index of suspicion for ARF in health care providers may be low due to decreasing incidence of the disease and clinical presentation that can mimic other conditions. We present the case of a 5-year-old boy with a history of intermittent fevers, fatigue, migratory joint pain, and weight loss following group A Streptococcus pharyngitis. The patient presented to the emergency department twice with the complaints described above. On his 3rd presentation, the workup for his symptoms revealed the diagnosis of acute rheumatic fever with severe mitral and aortic valve regurgitation. The patient was treated with penicillin G benzathine and was started on glucocorticoids for severe carditis. The patient was discharged with recommendations to continue secondary prophylaxis with penicillin G benzathine every 4 weeks for the next 10 years. This case illustrates importance of primary prevention of acute rheumatic fever with adequate antibiotic treatment of group A Streptococcus pharyngitis. Parents should also receive information and education that a child with a previous attack of ARF has higher risk for a recurrent attack of rheumatic fever. This can lead to development of severe rheumatic heart disease. Prevention of recurrent ARF requires continuous antimicrobial prophylaxis. Follow-up with a cardiologist every 1-2 years is essential to assess the heart for valve damage.

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    회원님의 원문열람 권한에 따라 열람이 불가능 할 수 있으며 권한이 없는 경우 해당 사이트의 정책에 따라 회원가입 및 유료구매가 필요할 수 있습니다.이동하는 사이트에서의 모든 정보이용은 NDSL과 무관합니다.

    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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  9. [해외논문]   Systemic Lupus Erythematosus-Related Pancreatitis in Children: Severe and Lethal Form  

    El Qadiry, R. (Pediatric B Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco ) , Bourrahouat, A. (Pediatric B Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco ) , Aitsab, I. (Pediatric B Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco ) , Sbihi, M. (Pediatric B Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco ) , Mouaffak, Y. (Pediatric ICU Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco ) , Moussair, F. Z. (Pediatric ICU Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco ) , Younous, S. (Pediatric ICU Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco)
    Case reports in pediatrics v.2018 ,pp. 1 - 4 , 2018 , 2090-6803 ,

    초록

    Systemic lupus erythematosus (SLE) is a chronic autoimmune inflammatory disease of unknown cause, characterized by multisystemic involvement. Its occurrence in children is rare, and acute pancreatitis is exceptional in this matter. Its diagnosis is clinical, biological, and radiological. Its treatment is based on corticosteroid therapy, and its progress is generally lethal. We report two cases of acute pancreatitis in the course of SLE, highlighting its life-threatening severity despite well-conducted treatment. Case 1 : 14-year-old patient, admitted to the pediatric ICU for altered state of consciousness. This child, an outpatient since 2009 for chronic arthralgia, was hospitalized five days previously in the pediatric ward for suspicion of severe SLE, before presenting abdominal pain and vomiting. Hyperlipasemia was found, and an abdominal CT scan confirmed the diagnosis of acute pancreatitis. The patient was put under immunosuppressive therapy composed of high-dosage of corticosteroid and cyclophosphamide cures. She died 20 days after her hospitalization by severe lupus flare with multiorgan failure. Case 2 : 14-year-old child, admitted to the Pediatric ward for prolonged fever associated with polyarthralgia (nondeforming, immovable, and additive) that had been progressing since 6 months with altered general state; his symptoms got worst 15 days before his hospitalization by having behavioral disorders and epigastralgia with vomiting. Pancreatitis was strongly suspected in the absence of improvement on symptomatic treatment and confirmed by hyperlipasemia 6 times the normal value and a swollen pancreas on the abdominal CT scan. The child was treated with Solumedrol and cyclophosphamide without improvement and then died after one month of hospitalization by a septic shock.

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    회원님의 원문열람 권한에 따라 열람이 불가능 할 수 있으며 권한이 없는 경우 해당 사이트의 정책에 따라 회원가입 및 유료구매가 필요할 수 있습니다.이동하는 사이트에서의 모든 정보이용은 NDSL과 무관합니다.

    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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  10. [해외논문]   Diagnosis of Systemic Lupus Erythematosus in a Polynesian Male with a History of Rheumatic Fever: A Case Report and Literature Review  

    Diaz, Charyse (Department of Pediatrics, University of Hawaii, John A. Burns School of Medicine, Kapi'olani Medical Center for Women and Children, Honolulu, HI 96826, USA ) , Lim, Matthew A. (Department of Pediatrics, University of Hawaii, John A. Burns School of Medicine, Kapi'olani Medical Center for Women and Children, Honolulu, HI 96826, USA ) , Liu, Chloe A. (Department of Pediatrics, University of Hawaii, John A. Burns School of Medicine, Kapi'olani Medical Center for Women and Children, Honolulu, HI 96826, USA ) , Miwa, Chloe S. (Department of Pediatrics, University of Hawaii, John A. Burns School of Medicine, Kapi'olani Medical Center for Women and Children, Honolulu, HI 96826, USA ) , Tokunaga, Darcy (Department of Pediatrics, University of Hawaii, John A. Burns School of Medicine, Kapi'olani Medical Center for Women and Children, Honolulu, HI 96826, USA ) , Hamamura, Faith D. (Department of Pediatrics, University of Hawaii, John A. Burns School of Medicine, Kapi'olani Medical Center for Women and Children, Honolulu, HI 96826, USA ) , Yamamoto, Kara (Department of Pediatrics, University of) , Kurahara, David
    Case reports in pediatrics v.2018 ,pp. 1 - 3 , 2018 , 2090-6803 ,

    초록

    The presence of rheumatic heart disease (RHD) and systemic lupus erythematosus (SLE) has rarely been described in one patient. This report describes an adolescent Polynesian male with RHD who developed SLE years later. Initially, he fulfilled modified Jones criteria for rheumatic fever with aortic insufficiency, transient arthritis, elevated streptococcal titers, and a high erythrocyte sedimentation rate with a negative antinuclear antibody (ANA). He responded well to nonsteroidal anti-inflammatory and penicillin prophylaxis, which supported the diagnosis of rheumatic fever. Five years after his RHD diagnosis, he developed pancreatitis with glomerulonephritis, nephrosis, and pancytopenia. In addition, laboratory results revealed that he had multiple autoantibodies: anti-Sm and extremely elevated anti-dsDNA and ANA, fulfilling diagnostic criteria for SLE. The patient was treated, and he responded to pulse steroids followed by oral steroid therapy. To our knowledge, there are no known reported cases of a patient who was diagnosed with both RHD and SLE and met the clinical criteria for both diseases. The rarity of this concurrent disease process in one patient suggests a possible overlap in humoral immunity toward self-antigens as well as ethnic variability that increases predisposition to rheumatologic diseases.

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