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Case reports in pediatrics 81건

  1. [해외논문]   A Wilms' Tumor with Spinal Cord Compression: An Extrarenal Origin?  

    Petit, Audrey (Département de Pédiatrique, CHU de Grenoble, Grenoble, France ) , Rubio, Amandine (Département de Pédiatrique, CHU de Grenoble, Grenoble, France ) , Durand, Chantal (Département de Radiologie, CHU de Grenoble, Grenoble, France ) , Piolat, Christian (Département de Chirurgie, CHU de Grenoble, Grenoble, France ) , Perret, Cé (Département de Pédiatrique, CHU de Grenoble, Grenoble, France ) , cile (Département de Pédiatrique, CHU de Grenoble, Grenoble, France ) , Pagnier, Anne (Département de Pédiatrique, CHU de Grenoble, Grenoble, France ) , Plantaz, Dominique (Département de Pathologie, CHU de Grenoble, Grenoble, France) , Sartelet, Hervé
    Case reports in pediatrics v.2018 ,pp. 1 - 4 , 2018 , 2090-6803 ,

    초록

    Spinal cord compression in Wilms' tumor (WT) is an extremely rare event that can have a very poor prognosis if not taken care of rapidly. Most cases reported in the literature involve widely metastatic patient with bone or paraspinal metastases or occasionally intradural metastasis. Here, we present the case of a 3-year-old girl of WT confirmed by biopsy, with spinal cord compression due to the direct contiguous spread of a tumor through 2 vertebral foramina. Abdominal ultrasonography and magnetic resonance imaging performed for an abdominal mass revealed a large heterogeneous tumor near the upper pole of the left kidney. A nodular infiltration extended through the T11-L1 and L1-L2 neural foramina, forming an intraspinal mass that compressed the spinal cord. Major paresthesia subsequently occurred, requiring urgent treatment with corticosteroids and chemotherapy. The evolution was rapidly satisfying. After six courses of chemotherapy, a left nephrectomy was performed. Macroscopic examination identified a large tumor attached to the kidney without renal infiltration. Microscopical examination concluded to a nephroblastoma with regressive changes, of intermediate risk. Evolution at 6 months is satisfactory, with no neurological deficit. The histological aspect of the tumor and the clinical outcome suggest that she had an extrarenal WT that spread through the vertebral foramina and was secondarily attached to the kidney.

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  2. [해외논문]   Congenital Granular Cell Tumor: Case Report and Review  

    Gardner, Preston (Department of Plastic & Reconstructive Surgery, Beaumont Hospital-Farmington Hills, 28050 Grand River Ave., Farmington Hills, MI 48336, USA ) , Rozzelle, Arlene (Department of Plastic & Reconstructive Surgery, Childrens Hospital of Michigan, Detroit Medical Center, 3901 Beaubien St., Detroit, MI 48201, USA)
    Case reports in pediatrics v.2018 ,pp. 1 - 3 , 2018 , 2090-6803 ,

    초록

    Congenital granular cell tumors are infrequently occurring masses occurring on a neonate's gingiva/alveolus. These lesions are benign with no noted malignant transformation, and treatment of excision is based on its effect on the neonate's respiratory ability and/or nutritional intake. The purpose of this review is to discuss a case of a congenital granular cell tumor and its treatment and review of the literature including demographics, histopathology, and operative treatment.

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    회원님의 원문열람 권한에 따라 열람이 불가능 할 수 있으며 권한이 없는 경우 해당 사이트의 정책에 따라 회원가입 및 유료구매가 필요할 수 있습니다.이동하는 사이트에서의 모든 정보이용은 NDSL과 무관합니다.

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  3. [해외논문]   Neuropsychiatric Disorder Associated with Group G Streptococcus Infection  

    Okumura, Rie (Department of Pediatrics, Niigata City General Hospital, Niigata, Japan ) , Yamazaki, Sawako (Department of Pediatrics, Niigata City General Hospital, Niigata, Japan ) , Ohashi, Tsukasa (Department of Child Neurology, Nishi-Niigata Chuo National Hospital, Niigata, Japan ) , Magara, Shinichi (Department of Child Neurology, Nishi-Niigata Chuo National Hospital, Niigata, Japan ) , Tohyama, Jun (Department of Child Neurology, Nishi-Niigata Chuo National Hospital, Niigata, Japan ) , Sakuma, Hiroshi (Department of Brain Development and Neural Regeneration, Tokyo Metropolitan Institute of Medical Science, Tokyo, Japan ) , Hayashi, Masaharu (School of Nursing, College of Nursing and Nutrition, Shukutoku University, Chiba, Japan ) , Saitoh, Akihiko (Department of Pediatrics, Niigata University, Niigata, Japan)
    Case reports in pediatrics v.2018 ,pp. 1 - 3 , 2018 , 2090-6803 ,

    초록

    Immune-mediated central nervous system manifestations of group A β -hemolytic Streptococcus (GABHS) infection include Sydenham's chorea, pediatric autoimmune neuropsychiatric disorders associated with streptococcal infection (PANDAS)-which includes tic and obsessive compulsive disorders-and a variety of neurobehavioral disorders. We report a case of Streptococcus dysgalactiae subspecies equisimilis (group G Streptococcus ) (GGS) infection associated with involuntary movements, complex tics, and emotional lability in an 11-year-old Japanese girl. Serum IgM and IgG antibodies to lysoganglioside were positive, and she responded rapidly to intravenous immunoglobulin treatment. Neuropsychiatric disorder associated with GGS infection was ultimately diagnosed. The present findings suggest that neuropsychiatric disorders can result from GGS infection and that the pathogenic mechanism is similar to that of GABHS infection. Future large-scale studies should examine the relation between GGS infection and onset of neuropsychiatric disorder.

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    회원님의 원문열람 권한에 따라 열람이 불가능 할 수 있으며 권한이 없는 경우 해당 사이트의 정책에 따라 회원가입 및 유료구매가 필요할 수 있습니다.이동하는 사이트에서의 모든 정보이용은 NDSL과 무관합니다.

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  4. [해외논문]   Acanthomatous Ameloblastoma of Mandible in a Paediatric Patient  

    Malathi, Narasimhan (Professor & Head, Department of Oral Pathology, Faculty of Dental Sciences, Sri Ramachandra Institute of Higher Education & Research (DU), Porur, Chennai, India ) , Giri, G. V. V. (Professor, Department of Oral & Maxillofacial Surgery, Faculty of Dental Sciences, Sri Ramachandra Institute of Higher Education & Research (DU), Porur, Chennai, India ) , Pandyan, Deepak A. (Assoc. Professor, Department of Oral &Maxillofacial Surgery, Faculty of Dental Sciences, Sri Ramachandra Institute of Higher Education & Research (DU), Porur, Chennai, India ) , Suganya, Ramalingam (Senior Lecturer in Oral Pathology, Department of Oral &Maxillofacial Surgery, Faculty of Dental Sciences, Sri Ramachandra Institute of Higher Education & Research (DU), Porur, Chennai, India ) , Thamizhchelvan, Harikrishnan (Professor, Department of Oral Pathology, Faculty of Dental Sciences, Sri Ramachandra Institute of Higher Education & Research (DU), Porur, Chennai, India)
    Case reports in pediatrics v.2018 ,pp. 1 - 4 , 2018 , 2090-6803 ,

    초록

    Ameloblastoma is a slow-growing, benign odontogenic tumor derived from odontogenic epithelial components with a mature fibrous stroma. It is the second most common odontogenic neoplasm following odontome. Acanthomatous ameloblastoma histologically presents with squamous epithelial metaplastic transformation of odontogenic tissue. The present case report of a 12-year-old male exclusively elaborates the issues concerned with the aggressive nature of acanthomatous ameloblastoma (AA) which is a distinctive variant of ameloblastoma.

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    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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  5. [해외논문]   Torticollis as Presentation for Atypical Kawasaki Disease Complicated by Giant Coronary Artery Aneurysms  

    Dyer, Tracey (Department of Pediatrics, Memorial University, 300 Prince Phillip Drive, St. John's, NL, Canada A1B 3V6 ) , Dancey, Paul (Department of Pediatrics, Memorial University, 300 Prince Phillip Drive, St. John's, NL, Canada A1B 3V6 ) , Martin, John (Department of Pediatrics, Memorial University, 300 Prince Phillip Drive, St. John's, NL, Canada A1B 3V6 ) , Shah, Suryakant (Department of Pediatrics, Memorial University, 300 Prince Phillip Drive, St. John's, NL, Canada A1B 3V6)
    Case reports in pediatrics v.2018 ,pp. 1 - 3 , 2018 , 2090-6803 ,

    초록

    Kawasaki disease (KD) is an acute systemic vasculitis of childhood. The diagnosis can be made in a patient who presents with a prolonged high fever and meeting at least four of five criteria including polymorphous rash, mucosal changes, extremity changes (including swelling and/or palmar and plantar erythema), bilateral nonsuppurative conjunctivitis, and unilateral cervical lymphadenopathy. Atypical KD refers to patients who have not met the full criteria and in whom atypical features may be present. We discuss a case of a 6-year-old male who presented to the Emergency Department with torticollis. A series of investigations for elevated inflammatory markers revealed dilated coronary artery aneurysms on echocardiogram, and thus he was diagnosed with atypical KD. His only other criteria were bilateral nonsuppurative conjunctivitis and a prior brief febrile illness. He was treated with high-dose intravenous immune globulin (IVIG) and low-dose aspirin. Low-molecular-weight heparin and atenolol were added due to the presence of giant aneurysms.

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    회원님의 원문열람 권한에 따라 열람이 불가능 할 수 있으며 권한이 없는 경우 해당 사이트의 정책에 따라 회원가입 및 유료구매가 필요할 수 있습니다.이동하는 사이트에서의 모든 정보이용은 NDSL과 무관합니다.

    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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  6. [해외논문]   Arterial Stiffness in a Toddler with Neurofibromatosis Type 1 and Refractory Hypertension  

    Stabouli, Stella (1st Department of Pediatrics, Aristotle University Thessaloniki, Hippokration Hospital, Thessaloniki, Greece ) , Vargiami, Euthymia (1st Department of Pediatrics, Aristotle University Thessaloniki, Hippokration Hospital, Thessaloniki, Greece ) , Maliachova, Olga (1st Department of Pediatrics, Aristotle University Thessaloniki, Hippokration Hospital, Thessaloniki, Greece ) , Printza, Nikoleta (1st Department of Pediatrics, Aristotle University Thessaloniki, Hippokration Hospital, Thessaloniki, Greece ) , Dotis, John (1st Department of Pediatrics, Aristotle University Thessaloniki, Hippokration Hospital, Thessaloniki, Greece ) , Kyriazi, Maria (1st Department of Pediatrics, Aristotle University Thessaloniki, Hippokration Hospital, Thessaloniki, Greece ) , Papazoglou, Konstantinos O. (5th Department of Surgery, Aristotle University of Thessaloniki, Hippokration Hospital, Thessaloniki, Greece ) , Zafeiriou, Dimitrios (1st Department of Pediatrics, Aristotle University Thessaloniki, Hippokration Hospital, Thessaloniki, Greece)
    Case reports in pediatrics v.2018 ,pp. 1 - 4 , 2018 , 2090-6803 ,

    초록

    Arterial hypertension is a common finding in patients with neurofibromatosis (NF) type 1. Renovascular hypertension due to renal artery stenosis or midaortic syndrome could be the underlying cause. We report the case of a 4-year-old girl with NF type 1 and midaortic syndrome whose changes in blood pressure and pulse wave velocity suggested the evolution of vasculopathy, diagnosis of renovascular hypertension, and provided insights of response to treatment. Hypertension persisted after percutaneous transluminal angioplasty in the abdominal aorta, requiring escalation of antihypertensive treatment, while arterial stiffness demonstrated a mild decrease. Regular assessment of blood pressure using ambulatory blood pressure monitoring and noninvasive assessment of arterial stiffness may enhance the medical care of patients with NF type 1.

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    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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  7. [해외논문]   Successful Management of Blue Rubber Bleb Nevus Syndrome (BRBNS) with Sirolimus  

    Ogu, Ugochi O. (Division of Hematology, Department of Oncology, Montefiore Medical Center, Bronx, NY, USA ) , Abusin, Ghada (Division of Pediatric Hematology/Oncology, Department of Pediatrics, University of Michigan, Ann Arbor, MI, USA ) , Abu-Arja, Rolla F. (Division of Pediatric Hematology/Oncology/BMT, Nationwide Children's Hospital, Columbus, OH, USA ) , Staber, Janice M. (Division of Pediatric Hematology/Oncology, Stead Family Department of Pediatrics, University of Iowa Carver College of Medicine, Iowa City, IA, USA)
    Case reports in pediatrics v.2018 ,pp. 1 - 5 , 2018 , 2090-6803 ,

    초록

    Blue rubber bleb nevus syndrome (BRBNS) is a rare disease with vascular malformations in several systems of the body, most commonly the skin and gastrointestinal tract. Bleeding from the gastrointestinal (GI) tract is a major complication, which may lead to chronic iron deficiency anemia and the need for frequent blood transfusions due to ongoing gastrointestinal blood loss. In this case report, we describe a now 19-year-old female with BRBNS who required six blood transfusions per year and after starting sirolimus is symptom- and transfusion-free.

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    회원님의 원문열람 권한에 따라 열람이 불가능 할 수 있으며 권한이 없는 경우 해당 사이트의 정책에 따라 회원가입 및 유료구매가 필요할 수 있습니다.이동하는 사이트에서의 모든 정보이용은 NDSL과 무관합니다.

    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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  8. [해외논문]   Hirschsprung's Associated Enterocolitis (HAEC) Personalized Treatment with Probiotics Based on Gene Sequencing Analysis of the Fecal Microbiome  

    Singer, Georg (Department of Paediatric and Adolescent Surgery, Medical University of Graz, Graz, Austria ) , Kashofer, Karl (Institute of Pathology, Medical University of Graz, Graz, Austria ) , Castellani, Christoph (Department of Paediatric and Adolescent Surgery, Medical University of Graz, Graz, Austria ) , Till, Holger (Department of Paediatric and Adolescent Surgery, Medical University of Graz, Graz, Austria)
    Case reports in pediatrics v.2018 ,pp. 1 - 6 , 2018 , 2090-6803 ,

    초록

    Approximately 40% of children with Hirschsprung's disease (HD) suffer from Hirschsprung's associated enterocolitis (HAEC) despite correct surgery. Disturbances of the intestinal microbiome may play a role. Treatment with probiotics based on individual analyses of the fecal microbiome has not been published for HD patients with recurrent HAEC yet. A boy with trisomy 21 received transanal pull-through at the age of 6 months for rectosigmoid HD. With four years, he suffered from recurrent episodes of HAEC. The fecal microbiome was measured during three healthy and three HAEC episodes by next-generation sequencing. The patient was started on daily probiotics for 3 months; the fecal microbiome was measured weekly. The fecal microbiome differed significantly between healthy and HAEC episodes. HAEC episodes were associated with significant decreases of Actinobacteria and significant increases of Bacteroidetes and Proteobacteria. Probiotic treatment led to a significant increase of alpha diversity and a significant increase of Bifidobacterium and Streptococcus as well as decreases of Rikenellaceae , Pseudobutyrivibrio , Blautia , and Lachnospiraceae . A longitudinal observation of the microbiome has never been performed following correction of Hirschsprung's disease. Probiotic treatment significantly changed the fecal microbiome; the alterations were not limited to strains contained in the administered probiotics.

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    NDSL에서는 해당 원문을 복사서비스하고 있습니다. 아래의 원문복사신청 또는 장바구니담기를 통하여 원문복사서비스 이용이 가능합니다.

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  9. [해외논문]   Use of Noninvasive Ventilation with Volume-Assured Pressure Support to Avoid Tracheostomy in Severe Obstructive Sleep Apnea  

    Diaz-Abad, Montserrat (Department of Medicine, University of Maryland School of Medicine, Baltimore, Maryland, USA ) , Isaiah, Amal (Department of Otorhinolaryngology-Head and Neck Surgery, University of Maryland School of Medicine, Baltimore, Maryland, USA ) , Rogers, Valerie E (Department of Family and Community Health, University of Maryland School of Nursing, Baltimore, Maryland, USA ) , Pereira, Kevin D. (Department of Otorhinolaryngology-Head and Neck Surgery, University of Maryland School of Medicine, Baltimore, Maryland, USA ) , Lasso-Pirot, Anayansi (Department of Pediatrics, University of Maryland School of Medicine, Baltimore, Maryland, USA)
    Case reports in pediatrics v.2018 ,pp. 1 - 4 , 2018 , 2090-6803 ,

    초록

    Obstructive sleep apnea (OSA) is a common disorder in children but can occasionally present with life-threatening hypoxemia. Obesity is a significant risk factor for poor outcomes of OSA treatment. Continuous positive airway pressure (CPAP) is indicated in children who are not candidates for or have an unsatisfactory response to adenotonsillectomy. Children acutely at risk for significant morbidity with other therapies are candidates for a tracheostomy. An eight-year-old patient with morbid obesity and severe OSA refractory to CPAP therapy was treated successfully with a novel noninvasive ventilation (NIV) mode with volume-assured pressure support (VAPS) and avoided tracheostomy.

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  10. [해외논문]   Systemic Lupus Erythematosus-Related Pancreatitis in Children: Severe and Lethal Form  

    El Qadiry, R. (Pediatric B Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco ) , Bourrahouat, A. (Pediatric B Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco ) , Aitsab, I. (Pediatric B Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco ) , Sbihi, M. (Pediatric B Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco ) , Mouaffak, Y. (Pediatric ICU Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco ) , Moussair, F. Z. (Pediatric ICU Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco ) , Younous, S. (Pediatric ICU Department, Mother-Child Pole, Mohammed VI University Hospital, Marrakesh, Morocco)
    Case reports in pediatrics v.2018 ,pp. 1 - 4 , 2018 , 2090-6803 ,

    초록

    Systemic lupus erythematosus (SLE) is a chronic autoimmune inflammatory disease of unknown cause, characterized by multisystemic involvement. Its occurrence in children is rare, and acute pancreatitis is exceptional in this matter. Its diagnosis is clinical, biological, and radiological. Its treatment is based on corticosteroid therapy, and its progress is generally lethal. We report two cases of acute pancreatitis in the course of SLE, highlighting its life-threatening severity despite well-conducted treatment. Case 1 : 14-year-old patient, admitted to the pediatric ICU for altered state of consciousness. This child, an outpatient since 2009 for chronic arthralgia, was hospitalized five days previously in the pediatric ward for suspicion of severe SLE, before presenting abdominal pain and vomiting. Hyperlipasemia was found, and an abdominal CT scan confirmed the diagnosis of acute pancreatitis. The patient was put under immunosuppressive therapy composed of high-dosage of corticosteroid and cyclophosphamide cures. She died 20 days after her hospitalization by severe lupus flare with multiorgan failure. Case 2 : 14-year-old child, admitted to the Pediatric ward for prolonged fever associated with polyarthralgia (nondeforming, immovable, and additive) that had been progressing since 6 months with altered general state; his symptoms got worst 15 days before his hospitalization by having behavioral disorders and epigastralgia with vomiting. Pancreatitis was strongly suspected in the absence of improvement on symptomatic treatment and confirmed by hyperlipasemia 6 times the normal value and a swollen pancreas on the abdominal CT scan. The child was treated with Solumedrol and cyclophosphamide without improvement and then died after one month of hospitalization by a septic shock.

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    Fig. 1 이미지

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